Paraparesis Secondary to Microscopic Polyangiitis Resistant to Corticosteroids. Report of a Case



 

Ignacio Saguier Padilla1*, Cinthya Reznik1, María Eugenia Conti1, Flavio Mercado1, Agustina Causillas2, Micaela Blanco2 and Ricardo Barcia2

1 División Neurología, Hospital de Clínicas José de San Martín, Buenos Aires, Argentina.

2 Medicina Interna, Sexta Cátedra, Hospital de Clinicas José de San Martín, Buenos Aires, Argentina.

*Corresponding Author: Ignacio Saguier Padilla, Third year resident, Neurology, Hospital de Clínicas José de San Martin, CABA, Argentina.

DOI: https://doi.org/10.58624/SVOANE.2023.04.0109

Received: October 10, 2023     Published: October 30, 2023

 

Abstract

Microscopic polyangiitis (MPA) is an ANCA-associated vasculitis. Almost half of the patients may present with involvement of the peripheral nervous system such as mononeuropathy or polyneuropathy. The initial treatment is with corticosteroids, and up to 30% are non-responders, where other treatments should be used. Rapidly progressive renal failure and intestinal ischemia are usually high-mortality complications.

Keywords: Microscopic polyangiitis, Mononeuritis multiplex, Resistance, Rapidly progressive renal failure.

Citation: Padilla IS, Reznik C, Conti ME, Mercado F, Causillas A, Blanco M, Barcia R. Paraparesis Secondary to Microscopic Polyangiitis Resistant to Corticosteroids. Report of a Case. SVOA Neurology 2023, 4:6, 179-183.