SVOA Neurology

Ruiz Navarrete PA^{* 1}, Ruiz Serrano L¹, León Ortega MT¹ and Galdón Castillo A¹

¹Video-EEG Unit. Clinical Neurophysiology Service, Virgen de las Nieves University Hospital, Granada, Spain

*CorrespondingAuthor: Dr. Pablo Airam Ruiz Navarrete, Virgen de las Nieves University Hospital, Clinical Neurophysiology Service AV. Juan Pablo II, 18013, Granada, Spain.

Received: March 14, 2022     Published: April 27, 2022

Abstract

Objective: To assess the usefulness of the electroencephalogram (EEG) as a support for the diagnosis of Moya-Moya disease in a pediatric patient. The most common symptom in pediatric age is transient ischemic attack produced in hyperventilation (HV).

Method: Study of a patient admitted for video-EEG monitoring (VEEG) in the Neurophysiology Unit of the Virgen de las Nieves University Hospital in Granada, with a bibliographic review in PubMed. 8-year-old patient with symptoms of focal seizures without loss of consciousness, with the semiology of left hypotonia and headache caused after HV. It is evaluated for a suspected diagnosis of an idiopathic epileptic seizure.

Results: VEEG is performed, showing two critical episodes associated with post-HV with right hemispheric slowing, compatible with the “re-build up” phenomenon Through EEG analysis, Moya-Moya disease was suspected and later confirmed by angiography.

Conclusion: EEG analysis is an appropriate predictive method of diagnosis and follow-up for pediatric Moya-Moya disease.

Significance: An EEG is a non-invasive, simple test that can be easily performed in the pediatric population. There are characteristic findings in the EEG such as the phenomenon of “re-build up” that occurs after HV and they help to secure a diagnosis.

Keywords: Moya-Moya disease, “re-build up” phenomenon, electroencephalogram, hyperventilation, pediatric.

Citation: Ruiz Navarrete PA, Ruiz Serrano L, Leon Ortega MT, Galdon Castillo A. “Video-EEG Findings in a Pediatric Patient with Moya-Moya Disease”. SVOA Neurology 3:3 (2022) Pages 85-90.