Unusual Presentation of Moyamoya Disease with Seizure and Syncope Successfully Managed with Magnesium Sulfate: A Case Report



Seyed Hamed Banihashem Rad1*, Hasan Birjandi2 and Feisal Rahimpour3*

1Department of Cardiology, Faculty of medicine, Mashhad University of Medical Sciences, Mashhad, Iran

2Assistant professor of pediatric Cardiology, Pediatric Department, Medical faculty, Mashhad University of Medical Sciences (MUMS), Mashhad, Iran

3Assistant professor of pediatric Cardiology, Pediatric Department, Medical faculty, Mashhad University of Medical Sciences (MUMS), Mashhad, Iran

*Corresponding Author: Feisal Rahimpour, MD, Assistant professor of pediatric Cardiology, Pediatric Department, Medical faculty, Mashhad University of Medical Sciences (MUMS), Mashhad, Iran.

Received: April 19, 2022     Published: May 09, 2022

 

Abstract

Idiopathic pulmonary hypertension is a rare lung vasculopathy with an unknown etiology. Moyamoya disease (MD) is characterized by diffuse distal intracranial stenosis. MD associated with pulmonary hypertension is a rare presentation. Here we report a child who presented with recurrent and intractable syncope and seizure that was diagnosed with MD with pulmonary hypertension. The episodes of syncope and seizure successfully reduced with administration of Magnesium sulfate and Sildenafil.

Keywords: moyamoya, syncope, pulmonary hypertension, pediatrics

Citation: Rad SHB, Birjandi H, Rahimpour F. “Unusual Presentation of Moyamoya Disease with Seizure and Syncope Successfully Managed with Magnesium Sulfate: A Case Report”. SVOA Paediatrics 2022, 1:3, 69-72.